Primary ciliary dyskinesia in children.

Authors

  • Rodica SELEVESTRU State University of Medicine and pharmacy "Nicolae Testemitanu" Pulmonology Clinic, Department of Pediatrics; IMSP Institute of Mother and Child
  • Veronica State University of Medicine and pharmacy "Nicolae Testemitanu" Pulmonology Clinic, Department of Pediatrics; IMSP Institute of Mother and Child
  • Alina LEAHU State University of Medicine and pharmacy "Nicolae Testemitanu" Pulmonology Clinic, Department of Pediatrics; IMSP Institute of Mother and Child
  • Svetlana SCIUCA State University of Medicine and pharmacy "Nicolae Testemitanu" Pulmonology Clinic, Department of Pediatrics; IMSP Institute of Mother and Child

DOI:

https://doi.org/10.52692/1857-0011.2021.3-71.51

Keywords:

ciliary dyskinesia, bronchiectasis, child

Abstract

Primary ciliary dyskinesia is characterized by impaired mucociliary clearance and contributes to the recurrence ofrecurrent and chronic upper and lower respiratory tract infections. In this paper we elucidated a clinical case confirmedin the Pneumology Clinic of the Institute of Mother and Child, where he was investigated by ECG, pulmonary Rg, pulmonary CT, saccharin test. Morbid history of persistent wet cough, mucopurulent sputum, nasal voice, difficult nasalbreathing. Radiography of the paranasal sinuses showed signs of pansinusitis. At pulmonary CT, there were characteristicsigns of chronic broncho-pulmonary processes - varicose and sac-shaped bronchiectasis, pleuro-pulmonary adhesions,fibro-atelectatic areas in various segments. Spirometry – moderate and severe restrictive and obstructive disorders.Key words: ciliary dyskinesia, bronchiectasis, child.

Author Biographies

Rodica SELEVESTRU, State University of Medicine and pharmacy "Nicolae Testemitanu" Pulmonology Clinic, Department of Pediatrics; IMSP Institute of Mother and Child

asist. universitar, dr.șt.med.

Veronica, State University of Medicine and pharmacy "Nicolae Testemitanu" Pulmonology Clinic, Department of Pediatrics; IMSP Institute of Mother and Child

medic resident pediatru

Alina LEAHU, State University of Medicine and pharmacy "Nicolae Testemitanu" Pulmonology Clinic, Department of Pediatrics; IMSP Institute of Mother and Child

medic resident pediatru

Svetlana SCIUCA, State University of Medicine and pharmacy "Nicolae Testemitanu" Pulmonology Clinic, Department of Pediatrics; IMSP Institute of Mother and Child

prof. universitar, dr.hab.șt.med.

References

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Published

2021-11-17

Issue

Section

Research Article