Ebstein anomaly. Retrospective study.

Abstract

Ebstein anomaly is a congenital heart malformation of the tricuspid valve and right ventricle. Surgical correction of Ebstein’s anomaly improves functional class and exercise tolerance, eliminates intracardiac right-to-left shunting (if present), and reduces the incidence of supraventricular tachyarrhythmias [3, 4, 6]. Due to the degree of variability of Ebstein’s Anomaly, correction is based on anatomical factors. In the case of unfavorable anatomical conditions, the replacement of the tricuspid valve is resorted to [3, 8]. The application of bidirectional cavopulmonary anastomosis is reserved for patients with poor right ventricular function [6, 9, 10]. Currently, overall early mortality after surgical correction in children and adults has decreased to less than 3% in experienced centers [4]. Surgical treatment of the symptomatic neonate remains a significant challenge, with approaches including either a biventricular correction or a univentricular correction. The given study is retrospective and reports the data on the incidence of the types according to the Carpentier classification, the severity and the surgical procedure applied for the correction of the anomaly [1, 9].